Squamous Cell Carcinoma With Hyper-IgE Syndrome: A Case Report


Sasihuseyinoglu A. S. , YILMAZ M. , ALTINTAŞ D. U. , DOĞRUEL D. , SERBES M. , Uguz A. H. , ...Daha Fazla

JOURNAL OF PEDIATRIC HEMATOLOGY ONCOLOGY, cilt.40, 2018 (SCI İndekslerine Giren Dergi) identifier identifier identifier

  • Cilt numarası: 40 Konu: 6
  • Basım Tarihi: 2018
  • Doi Numarası: 10.1097/mph.0000000000000954
  • Dergi Adı: JOURNAL OF PEDIATRIC HEMATOLOGY ONCOLOGY

Özet

Background: Hyper-immunoglobulin E syndrome (HIES) is a rare primary immunodeficiency disease characterized by recurrent infections and elevated levels of serum immunoglobulin E. usually over 2000 IU/mL. Recurrent and chronic infection of the epidermis and squamous epithelium may also be a cause of squamous cell carcinoma (SCC). SCC is rare with HIES.