Management of Facial Disfigurement in Orbitotemporal Neurofibromatosis


Coban-Karatas M., Altan-Yaycioglu R., Bal N., Akova Y. A.

OPHTHALMIC PLASTIC AND RECONSTRUCTIVE SURGERY, vol.26, no.2, pp.124-126, 2010 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 26 Issue: 2
  • Publication Date: 2010
  • Doi Number: 10.1097/iop.0b013e3181b8e4de
  • Title of Journal : OPHTHALMIC PLASTIC AND RECONSTRUCTIVE SURGERY
  • Page Numbers: pp.124-126

Abstract

A 19-year-old woman with type I neurofibromatosis requested reconstruction of her severe facial disfigurement caused by the plexiform neurofibroma of the right upper eyelid. Previously, she had glaucoma surgery for buphthalmus and enucleation with dermis fat transplantation. She was unable to wear prosthesis in the last year. Transverse palpebral resection of the lesion, lateral canthal reconstruction, and frontal sling ptosis surgery were performed at the same session. Postoperatively, the cosmetic appearance of the patient was markedly improved. No complication or progression was observed during 2 years follow-up. We believe that an individual based surgical plan may give acceptable results in these challenging cases.