Congenital Peribronchial Myofibroblastic Tumor: A Case Report and Review of the Literature


AÇIKALIN A. , GÜMÜRDÜLÜ D. , Bagir E., GÖNLÜŞEN G. , Iskit S.

BALKAN MEDICAL JOURNAL, cilt.30, ss.329-332, 2013 (SCI İndekslerine Giren Dergi) identifier identifier identifier

  • Cilt numarası: 30 Konu: 3
  • Basım Tarihi: 2013
  • Doi Numarası: 10.5152/balkanmedj.2013.8373
  • Dergi Adı: BALKAN MEDICAL JOURNAL
  • Sayfa Sayısı: ss.329-332

Özet

Background: Congenital peribronchial myofibroblastic tumor is a rare, solid mesenchymal tumor of the neonate, usually associated with non-immune hydrops fetalis.

Background: Congenital peribronchial myofibroblastic tumor is a rare, solid mesenchymal tumor of the neonate, usually associated with non-immune

hydrops fetalis.

Case Report: We present a case of congenital peribronchial myofibroblastic tumor, in whom a right lung mass was detected in intrauterine life. 12 days

after delivery by caesarean section, right lobectomy was performed. The tumor was limited to the lung, and was composed of spindle cells, proliferating

around a bronchial unit. Central necrosis and 4-5 mitoses per 10 high power fields were present. The patient is well 26 months after surgery.

Conclusion: We report this rare tumor with clinical, radiological and pathologic findings and a review of the literature