Congenital Peribronchial Myofibroblastic Tumor: A Case Report and Review of the Literature

AÇIKALIN A., GÜMÜRDÜLÜ D., Bagir E., GÖNLÜŞEN G., Iskit S.

BALKAN MEDICAL JOURNAL, vol.30, no.3, pp.329-332, 2013 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Review
  • Volume: 30 Issue: 3
  • Publication Date: 2013
  • Doi Number: 10.5152/balkanmedj.2013.8373
  • Journal Name: BALKAN MEDICAL JOURNAL
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus, TR DİZİN (ULAKBİM)
  • Page Numbers: pp.329-332
  • Çukurova University Affiliated: Yes

Abstract

Background: Congenital peribronchial myofibroblastic tumor is a rare, solid mesenchymal tumor of the neonate, usually associated with non-immune

hydrops fetalis.

Case Report: We present a case of congenital peribronchial myofibroblastic tumor, in whom a right lung mass was detected in intrauterine life. 12 days

after delivery by caesarean section, right lobectomy was performed. The tumor was limited to the lung, and was composed of spindle cells, proliferating

around a bronchial unit. Central necrosis and 4-5 mitoses per 10 high power fields were present. The patient is well 26 months after surgery.

Conclusion: We report this rare tumor with clinical, radiological and pathologic findings and a review of the literature

Background: Congenital peribronchial myofibroblastic tumor is a rare, solid mesenchymal tumor of the neonate, usually associated with non-immune hydrops fetalis.