JOURNAL OF CRANIOFACIAL SURGERY, cilt.18, sa.5, ss.1179-1182, 2007 (SCI-Expanded)
Ectodermal dysplasia (ED) is a group of disorders affecting ectodermal-derived tissues, mainly the skin and its appendages, including teeth, nails, hair, and sweat glands. Along with unusual and typical cramofacial findings, these patients present with a unique nasal deformity. This consists of wide nasal base, saddle nose deformity, lack of alar grooves, and wide nostrils. We present a case of ED in which the nasal deformity was treated with bilateral nasal osteotomies, costochondral cartilage graft to the dorsum, and reforming of alar grooves by suturing.