Correction of saddle nose deformity in ectodermal dysplasia


Acarturk T. O., Kivanc O.

JOURNAL OF CRANIOFACIAL SURGERY, vol.18, no.5, pp.1179-1182, 2007 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 18 Issue: 5
  • Publication Date: 2007
  • Doi Number: 10.1097/scs.0b013e31811ec1ca
  • Journal Name: JOURNAL OF CRANIOFACIAL SURGERY
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.1179-1182
  • Çukurova University Affiliated: No

Abstract

Ectodermal dysplasia (ED) is a group of disorders affecting ectodermal-derived tissues, mainly the skin and its appendages, including teeth, nails, hair, and sweat glands. Along with unusual and typical cramofacial findings, these patients present with a unique nasal deformity. This consists of wide nasal base, saddle nose deformity, lack of alar grooves, and wide nostrils. We present a case of ED in which the nasal deformity was treated with bilateral nasal osteotomies, costochondral cartilage graft to the dorsum, and reforming of alar grooves by suturing.