Correction of saddle nose deformity in ectodermal dysplasia


Acarturk T. O. , Kivanc O.

JOURNAL OF CRANIOFACIAL SURGERY, cilt.18, ss.1179-1182, 2007 (SCI İndekslerine Giren Dergi) identifier identifier identifier

  • Cilt numarası: 18 Konu: 5
  • Basım Tarihi: 2007
  • Doi Numarası: 10.1097/scs.0b013e31811ec1ca
  • Dergi Adı: JOURNAL OF CRANIOFACIAL SURGERY
  • Sayfa Sayısı: ss.1179-1182

Özet

Ectodermal dysplasia (ED) is a group of disorders affecting ectodermal-derived tissues, mainly the skin and its appendages, including teeth, nails, hair, and sweat glands. Along with unusual and typical cramofacial findings, these patients present with a unique nasal deformity. This consists of wide nasal base, saddle nose deformity, lack of alar grooves, and wide nostrils. We present a case of ED in which the nasal deformity was treated with bilateral nasal osteotomies, costochondral cartilage graft to the dorsum, and reforming of alar grooves by suturing.