Beta-thalassemia intermedia associated with moyamoya syndrome

Goksel B. K., Ozdogu H., Yildirim T., Oguzkurt L., Asma S.

JOURNAL OF CLINICAL NEUROSCIENCE, vol.17, no.7, pp.919-920, 2010 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 17 Issue: 7
  • Publication Date: 2010
  • Doi Number: 10.1016/j.jocn.2009.10.023
  • Journal Name: JOURNAL OF CLINICAL NEUROSCIENCE
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.919-920
  • Çukurova University Affiliated: No

Abstract

Moyamoya syndrome (MMS) is a progressive disorder. We report a 19-year-old boy with beta-thalassemia who presented with a left hemiparesis Brain MRI showed old middle cerebral artery and left frontal subcortical white matter infarcts Brain magnetic resonance angiography and digital subtraction angiography revealed occlusion of the bilateral internal carotid arteries with a rich network of basal collateral vessels To our knowledge this is the third report of beta-thalassemia intermedia and MMS, and the first report of a patient in Turkey It emphasizes the potential for cerebral infarct clue to anemia, protein S and thrombocytosis. (C) 2009 Elsevier Ltd All rights reserved