Beta-thalassemia intermedia associated with moyamoya syndrome


Goksel B. K. , Ozdogu H., Yildirim T., Oguzkurt L., Asma S.

JOURNAL OF CLINICAL NEUROSCIENCE, cilt.17, ss.919-920, 2010 (SCI İndekslerine Giren Dergi) identifier identifier identifier

  • Cilt numarası: 17 Konu: 7
  • Basım Tarihi: 2010
  • Doi Numarası: 10.1016/j.jocn.2009.10.023
  • Dergi Adı: JOURNAL OF CLINICAL NEUROSCIENCE
  • Sayfa Sayıları: ss.919-920

Özet

Moyamoya syndrome (MMS) is a progressive disorder. We report a 19-year-old boy with beta-thalassemia who presented with a left hemiparesis Brain MRI showed old middle cerebral artery and left frontal subcortical white matter infarcts Brain magnetic resonance angiography and digital subtraction angiography revealed occlusion of the bilateral internal carotid arteries with a rich network of basal collateral vessels To our knowledge this is the third report of beta-thalassemia intermedia and MMS, and the first report of a patient in Turkey It emphasizes the potential for cerebral infarct clue to anemia, protein S and thrombocytosis. (C) 2009 Elsevier Ltd All rights reserved