Thalassemia Major and Priapism: A Case Report of an Adolescent

OZ S., KÜPELİ S., Sezgin G., Bayram I.

JOURNAL OF PEDIATRIC HEMATOLOGY ONCOLOGY, vol.39, no.6, 2017 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 39 Issue: 6
  • Publication Date: 2017
  • Doi Number: 10.1097/mph.0000000000000846
  • Journal Name: JOURNAL OF PEDIATRIC HEMATOLOGY ONCOLOGY
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Keywords: thalassemia major, priapism, adolescent, RECURRENT PRIAPISM, INTERMEDIA, INHIBITORS
  • Çukurova University Affiliated: Yes

Abstract

Priapism is defined as a prolonged pathologic penile erection without sexual stimulation. In children, priapism secondary to sickle cell disease or hematological malignancy is a frequent condition. Appropriate treatment of priapism varies; the treatment is primarily etiological, conservative management. In the present report, we aimed to present a case of asplenic thalassemia major who developed priapism, improved with hydration and ibuprofen treatment. Clinicians should take into account that priapism can be encountered in patients with thalassemia major. To our knowledge this is the second publication reporting the association between thalassemia major and priapism in childhood.