Extra-Renal manifestations of atypical hemolytic uremic syndrome in children


Fidan K., Goknar N., GÜLHAN B., MELEK E. , Yildirim Z. Y. , Baskin E., et al.

PEDIATRIC NEPHROLOGY, cilt.33, ss.1395-1403, 2018 (SCI İndekslerine Giren Dergi) identifier identifier identifier

  • Cilt numarası: 33 Konu: 8
  • Basım Tarihi: 2018
  • Doi Numarası: 10.1007/s00467-018-3933-3
  • Dergi Adı: PEDIATRIC NEPHROLOGY
  • Sayfa Sayısı: ss.1395-1403

Özet

Atypical hemolytic uremic syndrome (aHUS) is a chronic disease characterized by thrombotic microangiopathy and a high risk of end-stage kidney disease. Dysregulation and/or excessive activation of the complement system results in thrombotic microangiopathy. Interest in extrarenal manifestations of aHUS is increasing. This study aimed to determine the clinical characteristics of patients with extrarenal manifestations of aHUS in childhood.