CUKUROVA MEDICAL JOURNAL, cilt.42, sa.2, ss.369-372, 2017 (ESCI)
Jarcho-Levin syndrome is associated with vertebra, central nervous system, cardiac, urinary and gastrointestinal system abnormalities. Incidence is 2.5/100000 and meningomyelocel and hydrocephalus is rare, in about 1/4 of the Jarcho-Levin cases. Patients die due to respiratory insufficiency. Here we present two cases of Jarcho-Levin syndrome operated for meningomyelocele and hydrocephalus.