Pseudotumor cerebri in a child with hyperimmunoglobulin E syndrome


İNCECİK F. , HERGUNER M. , ALTUNBAŞAK Ş. , YILMAZ M.

TURKISH JOURNAL OF PEDIATRICS, cilt.52, ss.546-547, 2010 (SCI İndekslerine Giren Dergi) identifier identifier identifier

  • Cilt numarası: 52 Konu: 5
  • Basım Tarihi: 2010
  • Dergi Adı: TURKISH JOURNAL OF PEDIATRICS
  • Sayfa Sayıları: ss.546-547

Özet

Hyperimmunoglobulin E syndrome (HIES) is recognized as a multisystem disorder with various connective tissue, skeletal and immunologic abnormalities. Central nervous system abnormalities have been considered a feature of HIES. Pseudotumor cerebri (PTC) is a condition characterized by increased intracranial pressure in the absence of any intracranial mass lesion or ventricular dilatation, with normal neurology and cerebral spinal fluid composition. PTC without papilledema is rarely reported in children. We describe an atypical presentation of PTC in a child with HIES.