Fibromuscular dysplasia (FMD) is a rare disorder characterized by multifocal stenosis with alternating dilations of the vessel segments, tubular narrowing, and wall outpouching and weblike stenosis. This report describes a young female patient who had an acute stroke associated with FMD. The aneiographic findings were typical of FMD, with bilateral carotid and brachiocephalic artery involvement: dissections in the aortic arch, the left subclavian artery, and the left common carotid artery, and 70% stenosis in the distal segment of the right common carotid artery: and an aneurysm in the ascending aorta. Although there are cases reported with FMD of the common carotid arteries and spontaneous dissections in the literature. aortic dissections and aneurysm of the ascending aorta are very rare in FMD.